Osteosarcoma Cancer from Detection to Treatment


What Is Osteosarcoma?

Osteosarcoma is a type of bone cancer that usually starts in the cells that form bones.

It most commonly occurs in the long bones of the arms and legs, especially near the knees and shoulders.

It is more common in children, teenagers, and young adults, but can occur at any age.


1. Initial Evaluation

Common Symptoms:
Persistent bone pain, especially at night or during activity
Swelling or lump around the affected bone
Reduced movement or limping
Fracture after minor injury
In advanced cases ➧ fatigue | weight loss | or fever

Common Sites:
Long bones ➧ distal femur | proximal tibia | proximal humerus
Less commonly ➧ pelvis | jaw | or spine


2. Physical Examination

Palpation of the affected area for swelling, tenderness, or warmth
Check for range of motion and neurovascular involvement
Examine nearby lymph nodes


3. Imaging and Scanning Tests

X-ray
Reveals classic “sunburst” appearance or Codman’s triangle.
Suggests malignancy ➧ further imaging needed.

Magnetic Resonance Imaging
Determines tumor size, local spread, and soft tissue involvement.
Essential for surgical planning.

CT Scan
Checks for lung metastases | most common site of spread.

Bone Scan | PET-CT
Detects metastases in other bones or distant sites.


4. Biopsy | Definitive Diagnosis

Types:
Core needle biopsy
Open surgical biopsy

Sample sent to pathology for:
Histological type
Grade
Molecular tests


5. Histologic Types

Conventional Osteosarcoma
Telangiectatic osteosarcoma
Small cell osteosarcoma
Parosteal osteosarcoma
Periosteal osteosarcoma


6. Staging | AJCC / Enneking System

IA - Low-grade tumor, localized
IB - Low-grade, extra-compartmental
IIA - High-grade, localized
IIB - High-grade, extra-compartmental
III - Metastatic disease


7. Multidisciplinary Treatment Planning

Team includes:
Orthopedic oncologist | surgery
Medical oncologist | chemotherapy
Radiologist
Pathologist
Physical therapist & rehabilitation team
Psychologist and nutritionist


8. Treatment Plan

Neoadjuvant Chemotherapy | Before Surgery

Purpose:
Shrink the tumor
Kill micrometastatic cells
Improve surgical outcomes

Common drugs:
Cisplatin + Doxorubicin | Adriamycin
High-dose Methotrexate with Leucovorin rescue
Ifosfamide + Etoposide

Usually given for 8-10 weeks before surgery.

Surgery | Main Treatment

Goal:
Remove entire tumor with clear margins.

Limb-Sparing Surgery:
Tumor removed and bone reconstructed with metal prosthesis, bone graft, or 3D-printed implant.

Amputation:
If tumor involves major nerves or blood vessels and limb cannot be preserved.

Rotationplasty:
Part of leg rotated and reattached to allow functional prosthesis use.

Surgeons confirm tumor-free margins

Adjuvant Chemotherapy | After Surgery

Purpose: destroy any remaining microscopic cancer cells.
Same drug combinations as pre-surgery for another 6–8 months.
Response is evaluated based on necrosis rate.

Radiation Therapy

Osteosarcoma is relatively radio-resistant, but radiation is used when:
Surgery cannot remove all tumor tissue.
Inoperable tumors.
Palliative treatment for pain relief in metastasis.

Targeted and Immunotherapy

Mifamurtide ➧ boosts immune system against osteosarcoma cells.
Denosumab.
Checkpoint inhibitors | PD-1 blockers | in trials for refractory cases.


9. Supportive and Rehabilitation Care

Pain management and psychological support.

Physiotherapy to regain limb function after surgery.

Nutritional support during chemo.

Prosthetic training | for amputees.

Fertility preservation counseling before chemotherapy.


10. Follow-up and Monitoring

After Treatment:
Every 3 months for first 2 years
Every 6 months for next 3 years
Annually after 5 years

Includes:
Physical exam
X-ray or MRI of surgical site
Chest CT for metastasis detection
Blood tests for drug toxicity